Hemorrhagic Reversible Cerebral Vasoconstriction Syndrome
نویسندگان
چکیده
The reversible cerebral vasoconstriction syndrome (RCVS) is well characterized as a group of conditions typically heralded by severe thunderclap headaches (TCH) associated with reversible segmental multifocal cerebral artery vasoconstriction. Approximately one third to half develop intracerebral hemorrhage (ICH), convexal subarachnoid hemorrhage (cSAH), ischemic stroke, and reversible brain edema (posterior reversible leukoencephalopathy syndrome or posterior reversible encephalopathy syndrome [PRES]), either alone or in combination. The pathophysiology of this syndrome is not known. It is unclear why some patients develop hemorrhagic lesions and others ischemic or edematous lesions. In a previous study, we showed that there were no significant differences between RCVS subgroups as defined by presumed risk factors and triggers, such as previous migraine and vasoconstrictive drugs. The aim of this study was to understand the mechanisms (the role of risk factors, triggers, and angiographic evolution) in hemorrhagic and nonhemorrhagic RCVS.
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